Allele-specific targeting of mutant ataxin-3 by antisense ...Cell Press
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Stefan Hauser, Jacob Helm, Melanie Kraft, Milena Korneck, Jeannette Hübener-. Schmid, and Ludger Schöls. Page Supplemental information. Supplementary ... Stefan Hauser, Jacob Helm, Melanie Kraft, Milena Korneck, Jeannette Hübener-. Schmid, and Ludger Schöls. Page Supplemental information. Supplementary ...
Evaluating noncoding nucleotide repeat expansions in ...Scholars Portal Journals
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Jeannette Hübener-Schmid · ORCID ID. Source Information. June 2023, Volume60(Issue6)Pages, p.3553To Molecular Neurobiology · PolyQ-expanded ataxin Jeannette Hübener-Schmid · ORCID ID. Source Information. June 2023, Volume60(Issue6)Pages, p.3553To Molecular Neurobiology · PolyQ-expanded ataxin
PolyQ‑expanded ataxin‑3 protein levels in peripheral blood ...
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Rieß, Jeannette Hübener-Schmid. Person(en), Gonsior, Kathrin (Verfasser) Kaucher, Gabriele Anna (Verfasser) Pelz, Patrik (Verfasser) Schumann, Dorothea ... Rieß, Jeannette Hübener-Schmid. Person(en), Gonsior, Kathrin (Verfasser) Kaucher, Gabriele Anna (Verfasser) Pelz, Patrik (Verfasser) Schumann, Dorothea ...
idn= Katalog der Deutschen NationalbibliothekDeutsche Nationalbibliothekvon J Hübener-Schmid · Zitiert von: 22 · 2013
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Polyglutamine-Expanded Ataxin-3: A Target Engagement Marker for Spinocerebellar Ataxia Type 3 in Peripheral Blood / Jeannette Hübener-Schmid, Kirsten ... Polyglutamine-Expanded Ataxin-3: A Target Engagement Marker for Spinocerebellar Ataxia Type 3 in Peripheral Blood / Jeannette Hübener-Schmid, Kirsten ...
Cerebellar soluble mutant ataxin-3 level decreases during disease...
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Full-text formats available: PDF, HTML, XML. AUTHORS. Huu Phuc Nguyen Jeannette Hübener Jonasz Jeremiasz Weber Stephan Grueninger Olaf Riess
Calpain-mediated ataxin-3 cleavage in the molecular ...
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von J Hübener · · Zitiert von: 118 — Calpain-mediated ataxin-3 cleavage in the molecular pathogenesis of spinocerebellar ataxia type 3 (SCA3). Jeannette Hübener ,. Jeannette Hübener ... von J Hübener · · Zitiert von: 118 — Calpain-mediated ataxin-3 cleavage in the molecular pathogenesis of spinocerebellar ataxia type 3 (SCA3). Jeannette Hübener ,. Jeannette Hübener ...
Polyglutamine‐Expanded Ataxin‐3
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von J Hübener-Schmid · · Zitiert von: 26 — Jeannette Hübener-Schmid, PhD,1,2*. Kirsten Kuhlbrodt, PhD,3 Julien Peladan, MSc,3. Jennifer Faber, MD,4,5 Magda M. Santana, PhD,6,7,8. Holger Hengel, MD,9,10. von J Hübener-Schmid · · Zitiert von: 26 — Jeannette Hübener-Schmid, PhD,1,2*. Kirsten Kuhlbrodt, PhD,3 Julien Peladan, MSc,3. Jennifer Faber, MD,4,5 Magda M. Santana, PhD,6,7,8. Holger Hengel, MD,9,10.
Polyglutamine-expanded ataxin-3: a target engagement marker for ...www.sciencegate.app › documents
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Jeannette Huebener-Schmid ◽. Kirsten Kuhlbrodt ◽. Julien Peladan ◽. Jennifer Faber ◽. Magda M Santana ◽ ... Keyword(s):. Gene Silencing ◽.
PolyQ-expanded ataxin-3 protein levels in peripheral blood ...
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von K Gonsior · · Zitiert von: 24 — ... Jeannette Hübener-Schmid (1). Afficher plus de détails. 1 Eberhard Karls Universität Tübingen = University of Tübingen 2 Universität Bonn = University of Bonn von K Gonsior · · Zitiert von: 24 — ... Jeannette Hübener-Schmid (1). Afficher plus de détails. 1 Eberhard Karls Universität Tübingen = University of Tübingen 2 Universität Bonn = University of Bonn
Dr. Jeannette Hübener - Gepris - DFGgepris.dfg.de/gepris/OCTOPUS?context=person&id= &task...
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Dr. Jeannette Hübener. Projekte. Als Antragstellerin abgeschlossene Projekte. Die Bedeutung der Calpain-abhängigen proteolytischen Spaltung von Ataxin-3 in ...
PolyQ-expanded ataxin-3 protein levels in peripheral blood ...Archive ouverte HAL
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... Jeannette Hübener-Schmid (1). Afficher plus de détails. 1 University of Tübingen 2 Universität Bonn = University of Bonn 3 DZNE - German Research Center for ...
Autophagy induction reduces mutant ataxin-3 levels and toxicity in a...
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Fiona M. Menzies,1 Jeannette Huebener,2 Maurizio Renna,1 Michael Bonin,2 Olaf Riess2 and. David C. Rubinsztein1. 1 Department of Medical Genetics, ...
Nuclear localization of ataxin-3 is required for the manifestation of...
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Allele-specific targeting of mutant ataxin-3 by antisense ...
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von S Hauser · · Zitiert von: 17 — ... Jeannette Hübener-Schmid,4 and Ludger Schöls1,2, *. Stefan Hauser. 1German Center for Neurodegenerative Diseases (DZNE), Tübingen, Germany. 2Hertie ... von S Hauser · · Zitiert von: 17 — ... Jeannette Hübener-Schmid,4 and Ludger Schöls1,2, *. Stefan Hauser. 1German Center for Neurodegenerative Diseases (DZNE), Tübingen, Germany. 2Hertie ...
Ataxin-3, The Spinocerebellar Ataxia Type ...
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Sowa, Eva Haas, Jeannette Hübener-Schmid, Axel Lorentz. View on publisher site Alert me about new mentions. X Demographics. Mendeley readers. Attention Score in ... Sowa, Eva Haas, Jeannette Hübener-Schmid, Axel Lorentz. View on publisher site Alert me about new mentions. X Demographics. Mendeley readers. Attention Score in ...
Cerebellar Soluble Mutant Ataxin-3 Level Decreases ...
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von HP Nguyen · · Zitiert von: 28 — Huu Phuc Nguyen, Jeannette Hübener, Jonasz Jeremiasz Weber, Stephan Grueninger, Olaf Riess, Andreas Weiss to Jeannette Hübener). The funders had no ... von HP Nguyen · · Zitiert von: 28 — Huu Phuc Nguyen, Jeannette Hübener, Jonasz Jeremiasz Weber, Stephan Grueninger, Olaf Riess, Andreas Weiss to Jeannette Hübener). The funders had no ...
Figure 5 from Calpain-mediated ataxin-3 cleavage in the ...
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Eva Haas +5 authors. Jeannette Hübener-Schmid. Medicine, Biology. Human molecular genetics TLDR. Lowering or removal of calpain-1 in cells or mice ... Eva Haas +5 authors. Jeannette Hübener-Schmid. Medicine, Biology. Human molecular genetics TLDR. Lowering or removal of calpain-1 in cells or mice ...
Johannes Gloeckner - Tübingen
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Nguyen, Jeannette Hübener-Schmid (2017) A combinatorial approach to identify calpain cleavage sites in the Machado-Joseph disease protein ataxin-3. Brain ... Nguyen, Jeannette Hübener-Schmid (2017) A combinatorial approach to identify calpain cleavage sites in the Machado-Joseph disease protein ataxin-3. Brain ...
Machado–Joseph disease/spinocerebellar ataxia type 3
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Ataxin-3, The Spinocerebellar Ataxia Type 3 Neurodegenerative Disorder Protein, Affects Mast Cell Functions · A. SowaEva HaasJeannette Hübener-SchmidA. Ataxin-3, The Spinocerebellar Ataxia Type 3 Neurodegenerative Disorder Protein, Affects Mast Cell Functions · A. SowaEva HaasJeannette Hübener-SchmidA.
Allele-specific targeting of mutant ataxin-3 by antisense PubMedpubmed.ncbi.nlm.nih.gov › ...
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vor 15 Stunden · Authors. Stefan Hauser , Jacob Helm , Melanie Kraft , Milena Korneck , Jeannette Hübener-Schmid , Ludger Schöls ...
Ataxia | PLOS ONE
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Cerebellar Soluble Mutant Ataxin-3 Level Decreases during Disease Progression in Spinocerebellar Ataxia Type 3 Mice. Huu Phuc Nguyen, Jeannette Hübener, [ .
A9169Sigma-Aldrich
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Jeannette Hübener et al. Brain : a journal of neurology, 134(Pt 7), ( ). Mutant ataxin-3 is aberrantly folded and ... Jeannette Hübener et al. Brain : a journal of neurology, 134(Pt 7), ( ). Mutant ataxin-3 is aberrantly folded and ...
Ataxin-3, The Spinocerebellar Ataxia Type 3 Neurodegenerative ...ouci.dntb.gov.ua › works
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von AS Sowa — Journal: Frontiers in Immunology, Publisher: Frontiers Media SA. Authors: Anna S. Sowa, Eva Haas, Jeannette Hübener-Schmid, Axel Lorentz ...
A Novel SCA3 Knock-in Mouse Model Mimics the Human SCA3 Disease...
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Spinocerebellar ataxia type 3 is the most common autosomal …nt inherited ataxia worldwide, caused by a CAG repeat expansion in the Ataxin-3 gene resulting...
Calpain-1 ablation partially rescues disease-associated hallmarks in...
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Eva Haas, Rana D. Incebacak, +9 authors Jeannette Hübener-Schmid. Biology TLDR. The novel Ataxin-3 knock-in mouse model shares neuropathological, ...
Autophagy induction reduces mutant ataxin-3 levels and toxicity in a...
pubmed.ncbi.nlm.nih.gov
Spinocerebellar ataxia type 3 is a neurodegenerative disorder caused by the expansion of the polyglutamine repeat region within the ataxin-3 protein. The...
Autophagy induction reduces mutant ataxin-3 levels and toxicity in a...
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Fiona M Menzies, Jeannette Huebener, Maurizio Renna, Michael Bonin, Olaf Riess, David C Rubinsztein. Index: Brain 133 (2010).
Cerebellar Soluble Mutant Ataxin-3 Level Decreases during Disease...
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Huu Phuc Nguyen ,. Contributed equally to this work with: Huu Phuc Nguyen, Jeannette Hübener. Affiliation Institute of Medical Genetics and Applied Genomics, ...
Establishing a TR-FRET based immunoassay to detect soluble ataxin-3...
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Establishing a TR-FRET based immunoassay to detect soluble ataxin-3 levels.
Johannes Gloeckner - Institute for Ophthalmic Researchwww.eye-tuebingen.de › ueffinglab › members › jo...
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... Jeannette Hübener-Schmid (2017) A combinatorial approach to identify calpain cleavage sites in the Machado-Joseph disease protein ataxin-3. Brain.
Identification of miR p as a novel prognostic biomarker ...
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— ... Ataxin-3: A Target Engagement Marker for Spinocerebellar Ataxia Type 3 in Peripheral Blood” by Jeannette Hübener-Schmid ... › ...
KPNB1 modulates the Machado–Joseph disease protein ataxin
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... Priscila Pereira Sena, Ana Velic, Maria Kalimeri, Rana Dilara Incebacak Eltemur, Jana Schmidt, Jeannette Hübener-Schmid, Stefan Hauser, Boris Macek, ... › catalog
PolyQ-expanded ataxin-3 protein levels in Archive ouverte HALhal.archives-ouvertes.fr › hal
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Alexandra Durr 4 Stefan Hauser 3, 1 Tim Rattay 3, 1 Matthis Synofzik 3, 1 Holger Hengel 3, 1 Ludger Schöls 3, 1 Olaf Rieß 1 Jeannette Hübener-Schmid 1
Verwandte Suchanfragen zu Jeannette Hübener
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